An adult with central cyanosis and differential pulmonary vascularity

Coarctation of the Aorta and a Parachute Mitral Valve in an Adult With Differential Cyanosis

Differential cyanosis may occur in Eisenmenger physiology in the presence of a patent ductus arteriosus (PDA). We present a unique case of a 22-year-old male manifesting as cyanosis of the left upper extremity and both lower extremities, but with preservation of the right upper extremity. Work-up revealed multiple congenital defects, reminiscent of the Shone's complex. Survival into adulthood i...

Cyanosis and pulmonary disease in infancy.

ease secondary to congenital heart disease. I woud like to show you two children, 0110 of whom was considered to have congenital heart disease and was found at postmortem examination to have primary pulmonary disease. In the other case the child was considered to have primary pulmonary disease and then was found to have pulmonary disease secondary to heart disease. The first case is that of a g...

Mitral stenosis with exertional cyanosis and pulmonary hemosiderosis.

A patient with mitral stenosis is reported who suffered from exertional cyanosis for the last eight years of his life. Radiologic examination of his chest demonstrated a diffuse pulmonary hemosiderosis, which was confirmed at autopsy. Physiologic studies in the last few weeks of life showed that the cyanosis was not due to impairment of oxygenation of the blood in the lungs but rather to slowed...

A Rare Case of Pulmonary Atresia with Ventricular Septal Defect with a Right Sided Aortic Arch and a Calcified Pulmonary AVM Presenting in an Adult without Cyanosis

Pulmonary atresia with ventricular septal defect (PA-VSD) with pulmonary arterial supply arising from the aorta representing large MAPCAs associated with a right sided aortic arch is an uncommon anomaly. Most of the patients succumb to severe respiratory compromise or congestive cardiac failure very early. We report the clinical details and imaging findings of a case of PA-VSD with a right side...

Pulmonary right-upper lobar arteriovenous fistula in an infant with progressive cyanosis.